González CAC, Corral CJC, González MTN, Vega MME

Idioma: Español
Referencias bibliográficas: 22
Paginas: 145-149
Archivo PDF: 156.01 Kb.

RESUMEN

La púrpura fulminante neonatal es una enfermedad grave y poco frecuente, causada por deficiencias congénitas o adquiridas de las proteínas C o S. Tiene alta mortalidad a menos que se realice el diagnóstico temprano y se inicie tratamiento. Describimos el caso de un recién nacido que comenzó de manera súbita, secundario a un infección intrahospitalaria por Acinetobacter junii, una dermatosis caracterizada por ampollas tensas, de contenido seroso y hemático, con evolución posterior a necrosis. Se documentó una deficiencia de proteína C transitoria. Recibió tratamiento con antibióticos, plasma fresco congelado y anticoagulación, con lo cual se recuperó totalmente.

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