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2006, Número 2

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Arch Cardiol Mex 2006; 76 (2)


Pentalogía de Cantrell. A propósito de un caso

Hernández-González M, Jiménez-Arteaga S, Ortega F, Solorio S, Martínez-Flores E, David-Gómez F, Sánchez-Soberanis A, Ortegón-Cerdeña J, López-Gallegos D, Argüero-Sánchez R, Alva C

Idioma: Español
Referencias bibliográficas: 37
Paginas: 202-207
Archivo PDF: 125.61 Kb.


RESUMEN

La ectopia cordis es una malformación congénita extremadamente rara, en donde el corazón está localizado total o parcialmente fuera de la cavidad torácica y que puede presentarse de forma aislada o asociada a otros defectos de la línea media. Cantrell y cols. en 1958 describieron por primera vez un síndrome raro que involucra defectos en la pared abdominal, el esternón, el diafragma, el pericardio y el corazón. Existen muy pocos casos operados con éxito. A continuación presentamos el caso de un paciente, en quien se integró el diagnóstico de esta pentalogía, cuya malformación congénita cardíaca es la presencia de un corazón univentricular con estenosis pulmonar y en quien se colocó una fístula de Blalock-Taussig clásica del lado izquierdo de forma exitosa y evolución satisfactoria.


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