Gómez RSL, Herrera AAR, Vega CV, Beltrán BY, Blanco DAT, Reyes SY

Language: Spanish
References: 7
Page: 105-108
PDF size: 465.84 Kb.

ABSTRACT

Fibrous dysplasia is a rare benign disease where there is a disorder in the maturation of the bone mesenchyme, which is replaced by abnormal fibrous tissue, the result of a sporadic gene mutation in the Gsα protein activator gene GNAS1. There is a monostotic and a polyostotic form that when associated with endocrine disorders and hyperpigmentation in the skin is called McCune-Albright syndrome. With the aim of demonstrating the importance of the early diagnosis of Polyostotic Fibrous Dysplasia for the prevention of complications, a 34-year-old male patient, male, white, suffered from a slight trauma to the left arm. humerus fracture. The interrogation revealed a history of multiple fractures in the same place. The physical examination revealed pain in the area of the trauma and limitation of movements. Indexing.

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