De Miguel-Ibáñez R, Sánchez-González MD, Herrera-Madrid DA

Language: Spanish
References: 8
Page: 121-126
PDF size: 260.35 Kb.

ABSTRACT

Background: Chronic myeloid leukemia is a myeloproliferative neoplasm with a median age of diagnosis in Mexico of 40 years. The initial manifestations are varied; however, priapism is a very rare entity associated to chronic myeloid leukemia.
Clinical case: An 18-year-old male with an 8-hour episode of ischemic priapism managed with cavernous lavage, achieving complete flaccidity of the penis. The patient was diagnosed with chronic myeloid leukemia, initiating cytoreduction with hydroxycarbamide and after having molecular confirmation, we started treatment with a tyrosine kinase inhibitor. The patient was discharged in excellent conditions, without sequelae of erectile dysfunction, all this attributed to the time of evolution, the adequate management of the urological emergency and the prompt identification and treatment of the precipitating condition.
Conclusions: It is important to do the proper diagnostic and therapeutic approach in young patients attending to the emergency department with priapism because the cause may be underestimated and delay the treatment of the underlying cause, having as a result a poor prognosis.

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