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Boletín Clínico de la Asociación Médica del Hospital Infantil del Estado de Sonora

2022, Number 2

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Bol Clin Hosp Infant Edo Son 2022; 39 (2)

Jodhpur disease. Presentation of a rare clinical case of gastric outlet obstruction and review of the literature

Quero-Hernández A, Gómez-Márquez KL, Garzón-Sánchez E, Reyes-Gómez U, Reyes-Hernández KL, Quero-Estrada A, López-Cruz G, Álvarez-Solís RM, Vargas-Mosso ME, Hernández-Lira I, Reyes-Hernández MU, Matos-Alviso LJ, de Lara-Huerta J

Language: Spanish
References: 15
Page: 68-72
PDF size: 233.00 Kb.


ABSTRACT

Jodhpur disease is characterized by projectile and gastric content vomiting, visible gastric peristalsis, weight loss and dehydration, without apparent cause, accompanied by electrolyte disturbances, acid-base imbalance. The objective is to describe a case of Jodhpur disease resolved with Jaboulay pyloroplasty. A 2-yearold female, who 2 weeks prior to her admission with vomiting of gastric content, not biliary, on a number of 8 occasions a day, and who due to dehydration and electrolyte disorder was treated with parenteral solutions on several occasions. Due to the persistence of non-bilious vomiting, she is referred to our institution, with severe dehydration. Panendoscopy is performed and gastromegaly, fundus mucosa and normal antrum and pyloric obstruction are observed. She is treated with Jaboulay-type pyloroplasty and is discharged 8 days later. Jodhpur disease is a disorder that presents obstruction to the gastric outlet tract, which occurs in childhood and even in adolescence with the absence of histopathological alterations and causes not yet known. We believe that panendoscopy is the resource that will allow us to establish the diagnosis and solve the problem of primary and acquired gastric outlet obstruction with pyloroplasty.


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