González RLA, González RCA, Guerrero VAF

Language: Spanish
References: 15
Page: 81-86
PDF size: 232.55 Kb.

ABSTRACT

We present the clinical case of a young toodler with heart disease called Lutembacher syndrome associated with the presence of a ductus arteriosus. The Lutembacher syndrome is defined by the presence of mitral valve disease and secundum-type atrial septal defect. The diagnosis of this anomaly was done by echocardiography where the mentioned structural anomalies were evidenced also the presence of severe pulmonary hypertension due to secondary hemodynamic deterioration was shown. Clinical manifestation of heart failure and radiological cardiomegaly occurred upon admission to the hospital. As Lutembacher Syndrome is extremely rare in children, with only a few isolated cases published, we consider its publication to be of interest.

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