Otorhinolaryngological manifestations of a rare hematological disease: Blastic plasmacytoid dendritic cell neoplasm

Luis Miguel Méndez Saucedo; Natalia Montemayor Peña; Ana Lilia Ramírez Maldonado; Abraham Hernández Mundo; Francisco Javier Mancilla Mejía; Laura Serrano Salinas

2023, Number 2

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Rev Hematol Mex 2023; 24 (2)

Otorhinolaryngological manifestations of a rare hematological disease: Blastic plasmacytoid dendritic cell neoplasm

Méndez SLM, Montemayor PN, Ramírez MAL, Hernández MA, Mancilla MFJ, Serrano SL

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Language: Spanish
References: 6
Page: 101-105
PDF size: 279.07 Kb.

ABSTRACT

Background: Plasmacytoid blast neoplasm is rare, predominates in men. Clinically, skin lesions are manifested, with no report of compromised airway mucosa.
Clinical case: This paper reports two documented clinical cases with affection of airway mucosa, CD123 positive, in which the diagnosis of blastic plasmacytoid dendritic cell neoplasia was confirmed.
Conclusions: Blastic plasmacytoid dendritic cell neoplasia is an underdiagnosed disease because the clinical presentation can be confused with other hematological or dermatological diseases. In patients with lesions in the airway mucosa, it is necessary to consider this hematological disease.

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