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ISSN 2448-5640 (Print)
Diario Oficial de la Sociedad Mexicana de Cirugía Cardiaca, A.C., y del Colegio Mexicano de Cirugía Cardiovascular y Torácica, A.C.

2022, Number 4

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Cir Card Mex 2022; 7 (4)

Aortic valve replacement in pediatric patients with Laubry-Pezzi syndrome

Ortega-Zhindón DB, Flores-Sarria IP, Calderón-Colmenero J, García-Montes JA, Pereira-López GI, Cervantes-Salazar JL

Language: English
References: 12
Page: 70-73
PDF size: 259.03 Kb.


ABSTRACT

Objective. The aim was to evaluate the clinical and surgical results of pediatric patients with Laubry - Pezzi Syndrome (LPS) undergoing cardiac surgery. Methods. An observational and retrospective study was carried out. Patients diagnosed with LPS undergoing cardiac surgery from January 1, 2004 and March 31, 2021, were included; preoperative characteristics and conditions were considered. Results. Six patients were included, with a mean age of 16.3 ± 0.8 years, being 66.7% women. Had a previous surgery 33%. In 83.3% of the cases, mechanical aortic prostheses were used, with an average size of 23 ± 0.8 mm. Perioperative complications included arrhythmias (83.3%), pleural effusion (83.3%), and major bleeding (16.7%). Overall survival was 66.7% and 16.7% reoperation. Conclusions. The closure of the ventricular defect and replacement of the aortic valve in pediatric patients with LPS provides a therapeutic option in patients where aortic valve repair is not possible or has been unsuccessful.


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