Martínez-Félix NS, Cabanillas-Ayón M, Escamilla-Salazar FD, Moreno-Gómez R, Aguirre-Flores E, Zatarain-Bayliss I

Language: Spanish
References: 11
Page: 51-55
PDF size: 304.16 Kb.

ABSTRACT

Scimitar syndrome is a congenital cardiac malformation, not so frequent, constituting 0.5 to 2% of congenital heart disease and 3 to 5% of cases of anomalous return of pulmonary veins. It is caused by a defect in the embryological development of the pulmonary venous sinus, which conditions the persistence of aberrant pulmonary veins. It is characterized by the presence of an anomalous drainage of the pulmonary veins, which through the inferior vena cava is directed to the right atrium. Clinically, it presents very variably, from asymptomatic to severe heart failure, with tachypnea being the most frequently associated clinical manifestation and whose unspecificity makes diagnosis difficult; characteristics such as age at presentation and the malformations that usually coexist with this syndrome are the main determinants of the severity of the manifestations.
In this paper we describe the case of a neonate carrier of scimitar syndrome, with emphasis on the apparently benign clinical evolution and the protocol required for diagnostic determination.

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