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ISSN 1025-0255 (Electronic)

2022, Number 1

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AMC 2022; 26 (1)

Pierre Robin's malformative sequence

Rodríguez-Díaz AM, Rodríguez-Díaz LK, Taboada-Lugo N, Navas-Toledo A

Language: Spanish
References: 19
Page:
PDF size: 563.90 Kb.


ABSTRACT

Introduction: The Pierre Robin’s malformative sequence is clinically characterized by micrognathia, glossoptosis, upper airway obstruction and frequently cleft palate, which can be life-threatening.
Objective: To present a case of a newborn diagnosed with the Pierre Robin's malformative sequence attended at the Mariana Grajales Gyneco-Obstetric University Hospital of the Villa Clara province.
Case report: A white female patient, term and low weight was attended. A marked micrognathism and retrogmatism is observed in neonatal physical examination, oral examination showed glossoptosis, and palatine fissure, dysmorphic pattern typical of Pierre Robin’s malformative sequence. The neonate was evaluated by different specialties. Conservative treatment was indicated through the prone position and enteral bottle feeding in a semi-seated position, placement of palatal plate and follow-up by consultation of the specialities involved. The patient left the hospital with a satisfactory evolution.
Conclusions: With conservative treatment and interdisciplinary participation of different medical and dentistry specialties a satisfactory result is achieved in the neonate.


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