medigraphic.com
ISSN 1561-2937 (Print)

2022, Number 4

<< Back

Rev Cubana Cardiol Cir Cardiovasc 2022; 28 (4)

A controversial cardiomyopathy: a case report

Jerez CAM, Andalia PK, Guevara MG, Borges MYR, Martínez CA, Valdés MA

Language: Spanish
References: 14
Page: 1-5
PDF size: 379.50 Kb.


ABSTRACT

Challenging cardiomyopathies in their genesis, evolution and therapeutic conduct, which have heart failure with its complexities as a common syndrome, are updated annually. We describe the case of a 46 year-old male patient with a history of heart failure of eight years of evolution, debut symptom, significant weight loss, dyspnea on small efforts, asthenia, nocturnal cough and edema in the lower limbs. After clinical stabilization and pharmacological optimization, the echocardiogram documented the diagnosis of biventricular noncompaction cardiomyopathy, unfortunately not corroborated by cardiac magnetic resonance due to the death of the patient. This is a rare disease and its diagnostic protocols are currently under debate; however, the multimodality of the images and an exhaustive clinical approach can define its diagnosis. The case presented, although rare, deserves review and its handling, both diagnostic and therapeutic, is a relevant contribution to modern cardiology.


REFERENCES

  1. Álvarez Zenteno P, Meza Peñafiel L, Aroca Del Río P. Miocardiopatía no compactada y restrictiva en pediatría: Dos tipos de enfermedades del miocardio que son importantes saber reconocer. Andes pediátrica. 2021 [acceso 30/04/2022];92(5):667-76. Disponible en: http://www.scielo.cl/scielo.php?script=sci_abstract&pid=S2452-60532021000500667&lng=es&nrm=iso&tlng=p

  2. Moncayo PQ, Loja BÁ, Pesantez SV, Espinoza DC. Reporte de Caso: Miocardiopatía No compactada en paciente con Insuficiencia Cardíaca. Metro Ciencia. 2021 [acceso 30/04/2022];29(suppl 2):120-2. Disponible en: https://www.revistametrociencia.com.ec/index.php/revista/article/view/391

  3. Lozano DS, Vílchez FG, Lozano DS, Vílchez FG. Miocardiopatía no compactada. Revista Uruguaya de Cardiología. 2019 [acceso 30/04/2022];34(1):284-306. Disponible en: http://www.scielo.edu.uy/scielo.php?script=sci_abstract&pid=S1688-04202019000100284&lng=es&nrm=iso&tlng=es

  4. Ikeda U, Minamisawa M, Koyama J. Isolated left ventricular non-compaction cardiomyopathy in adults. Journal of Cardiology. 2015 [acceso 22/05/2022];65(2):91-7. Disponible en: https://linkinghub.elsevier.com/retrieve/pii/S0914508714002974

  5. Aras D, Tufekcioglu O, Ergun K, Ozeke O, Yildiz A, Topaloglu S, et al. Clinical features of isolated ventricular noncompaction in adults long-term clinical course, echocardiographic properties, and predictors of left ventricular failure. Journal of Cardiac Failure. 2006 [acceso 22/05/2022];12(9):726-33. Disponible en: https://linkinghub.elsevier.com/retrieve/pii/S1071916406008566

  6. Van Waning JI, Moesker J, Heijsman D, Boersma E, Majoor‐Krakauer D. Systematic review of genotype‐phenotype Correlations in Noncompaction Cardiomyopathy. Jam Heart Assoc. 2019 Dec 3;8(23): e012993. doi: 10.1161/JAHA. 119.012993. Epub 2019 Nov 27. PMID: 31771441; PMCID: PMC6912966 Disponible en: https://www.ahajournals.org/doi/10.1161/JAHA.119.012993

  7. Chin TK, Perloff JK, Williams RG, Jue K, Mohrmann R. Isolated noncompaction of left ventricular myocardium. A study of eight cases. Circulation. 1990 [acceso 22/05/2022];82(2):507-13. Disponible en: https://www.ahajournals.org/doi/10.1161/01.CIR.82.2.507

  8. Yin L. Non-Compact Cardiomyopathy or Ventricular Non-Compact Syndrome? J Cardiovasc Ultrasound. 2014 [acceso 22/05/2022];22(4):165. Disponible en: https://e-jcvi.org/DOIx.php?id=10.4250/jcu.2014.22.4.165

  9. Pasotti M. The MOGE(S) Classification for a Phenotype-Genotype Nomenclature of Cardiomyopathy. Journal of the American College of Cardiology. 2014 [acceso 22/05/2022];63(23):2584. Disponible en: https://linkinghub.elsevier.com/retrieve/pii/S0735109714019950

  10. Towbin JA, Ballweg J, Johnson J. Left Ventricular Noncompaction Cardiomyopathy. En: Heart Failure in the Child and Young Adult. Elsevier. 2018 [acceso 22/05/2022]: 269-90. Disponible en: https://linkinghub.elsevier.com/retrieve/pii/B978012802393800020X

  11. Zemrak F, Ahlman MA, Captur G, Mohiddin SA, Kawel-Boehm N, Prince MR, et al. The relationship of left ventricular trabeculation to ventricular function and structure over a 9.5-year follow-up. Journal of the American College of Cardiology. 2014 [acceso 22/05/2022];64(19):1971-80. Disponible en: https://linkinghub.elsevier.com/retrieve/pii/S0735109714061531

  12. Stanton C, Bruce C, Connolly H, Brady P, Syed I, Hodge D, et al. Isolated left ventricular noncompaction syndrome. The American Journal of Cardiology. 2009 [acceso 22/05/2022];104(8):1135-8. Disponible en: https://linkinghub.elsevier.com/retrieve/pii/S0002914909011862

  13. Aung N, Doimo S, Ricci F, Sanghvi MM, Pedrosa C, Woodbridge SP, et al. Prognostic significance of left ventricular noncompaction: systematic review and meta-analysis of observational studies. Circ Cardiovascular Imaging. 2020 [acceso 22/05/2022];13(1):e009712. Disponible en: https://www.ahajournals.org/doi/10.1161/CIRCIMAGING.119.009712

  14. Cuevas J, Ptaszynski R, Cigarrán H, Calvo J, Martín M. Left ventricular noncompaction cardiomyopathy: Recent advances. Kardiologia Polska (Polish Heart Journal). Vol 80, No (2022) Disponible en: https://journals.viamedica.pl/kardiologia_polska/article/view/KP.a2022.0089




2020     |     www.medigraphic.com