Ortiz GJL, Larita CE

Language: Spanish
References: 6
Page: 39-41
PDF size: 380.93 Kb.

ABSTRACT

Noonan syndrome is a disease of autosomal dominant origin, with a high incidence rate, among its fundamental manifestations are short stature, congenital heart disease and a characteristic facial phenotype. A 22-year-old patient came accompanied by his mother for dental consultation due to a fracture of the lingual side of the 36th dental organ. On interrogation the mother refers that her son suffers from Noonan Syndrome, which is corroborated by the facial features of the patient who at all times is cooperative.

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