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Órgano Oficial de difusión científica de la Asociación Mexicana de Cirujanos de Columna A. C.

2025, Number 2

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Cir Columna 2025; 3 (2)

Extraosseous intradural extramedular Ewing sarcoma: case report

Tamayo-Gómez CD, Rodríguez-Messina A, Robles-Ortiz RE, Sosa-Rascón OM, Ramírez-Hernández F, Tamayo-Gómez ME

Language: Spanish
References: 22
Page: 126-132
PDF size: 337.19 Kb.


ABSTRACT

Ewing sarcoma (ES) is a malignant tumor that generally occurs in pediatric males. Its location in the neck is rare, with extraosseous presentation in this area being exceptional (3.4%), even more if it is extramedullary intradural. The presence of non-specific clinical symptoms makes early detection difficult, which tends to occur when the tumor causes spinal cord involvement, requiring an urgent surgical approach. We present the case of a 49-year-old female patient with neck pain of two years' duration, who after a symptomatic exacerbation lasting one month, presented right hemiparesis and loss of sphincter control. Diagnostic approach with magnetic resonance imaging showed multidirectional bulging of the annulus fibrosus measuring 300 × 300 × 100 mm, located at C3-T1 that compressed the dural sac plus bilateral neural foraminal involvement. Surgical management through a posterior cervical approach plus stabilization of lateral masses from C3 to C7, with a histopathological report of Ewing sarcoma complemented by detection of the t(11;22)(q24;q12) translocation of EWSR1. After surgery, the patient showed improvement with independence in work activity and daily life.


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