2026, Number 4
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Acta Med 2026; 24 (4)
Retroperitoneal fibrosarcoma, uncommon diagnosis
Funes RJF, Tinoco TL, Funes CME, Funes CFP
Language: Spanish
References: 5
Page: 446-448
PDF size: 2145.58 Kb.
ABSTRACT
Introduction: soft-tissue sarcomas are exceedingly rare,
accounting for < 1% of all adult malignancies. Sarcomatous
tumors are located within the retroperitoneum in < 10% of
cases.
Case report: 51-year-old male, with no history, with
a three-month history of moderate diffuse abdominal pain,
without asthenia, adynamic, anorexia, or weight loss, detecting
a large abdominal mass, the computed tomography showed
a retroperitoneal mass of 33 × 29 × 23 cm. Surgery was
performed for its total removal, corresponding to fibrosarcoma
with a weight of 13,800 g.
Conclusions: standard treatment
has become upfront primary surgical resection for most
subtypes. Radiation and systematic therapy have a limited role.
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