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2007, Number 4

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Med Cutan Iber Lat Am 2007; 35 (4)

Papular mucinosis: uncommon presentation of amyopathic dermatomyositis

Widholzer RMC, Dazzi PB, Rockenbach M, Bernardes SC, Furian R, Libis AS, Bonamigo RR
Full text How to cite this article

Language: Portugu?s
References: 14
Page: 189-192
PDF size: 249.00 Kb.


Key words:

papular mucinosis, dermatomyositis, amyopathic.

ABSTRACT

The authors report a case of amyopathic dermatomyositis with uncommon papular mucinosis. The dermatomyositis diagnosis was based on clinical findings and skin biopsy and amyophathic presentation was defined by no clinical evidence of muscle weakness, normal laboratory results, electromyogram and muscle biopsy. Amyopathic dermatomyositis is a rare subtype of the disease. A prompt diagnosis of dermatomyositis depends on recognition of classic cutaneous findings and rare presentations such as papular mucinosis. An accurate patient diagnosis contributes for the correct treatment.


REFERENCES

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  2. 2.Stonecipher, et al. Cutaneous changes of dermatomyositis in patients with normal muscle enzymes: Dermatomyositis sine myositis? J Am Acad Dermatol 1993;28:951-6.

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  5. 5.Tan, Tan and Ng. Cutaneous mucinosis in dermatomyositis associated with a malignant tumor. J Am Acad Dermatol 2003;48:S41-2.

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  8. Callen JP. Collagen vascular diseases. J Am Acad Dermatol 2004;51:427-39.

  9. Dawkins, et al. Dermatomyositis: A dermatology-based case series. J Am Acad Dermatol 1998;38:397-404.

  10. Sontheimer RD. Cutaneous features of classic dermatomyositis and amyopathic dermatomyositis. Curr Opin Rheumatol 1999;11:475-482.

  11. 11.Erel A, et al. Amyopathic dermatomyositis. Int J Dermatol 2000;39:760-773.

  12. Euwer RL, Sontheimer RD. Amyopsthic dermatomyositis (dermatomyositis siné myosites). J Am Acad Dermatol 1991;24:959-66.

  13. 13.Callen JP. The value of malignancy evaluation in patients with dermatomyositis. J Am Acad Dermatol 1982;6:253-9.

  14. Woo TY, Callen JP, et al. Cutaneous lesions of dermatomyositis are improved by hydroxychloroquine. J Am Acad Dermatol 1984;10:592-600.




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Med Cutan Iber Lat Am. 2007;35