2003, Number 1
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ABSTRACTObjective: To inform on two patients, one with adult polycystic liver disease and the other with a hepatobiliary cystadenoma and mesenchymal stroma.
Setting: Third level health care hospital.
Description of the cases: Patient 1. Woman, 71 years old, with a disorder of 3 months of evolution characterized by pain in the right hypochondrium and sensation of heaviness. The abdominal tomography revealed hepatic cystic lesions, the largest in the left lobule, 15 cm in diameter. Cholangiography revealed that the cysts did not communicate with the biliary trunk. She was subjected to surgery, performing resection of the largest cyst and cholecystectomy. Histopathological diagnosis: Adult polycystic liver disease. Resection of an 11-cm cyst.
Patient 2. Woman, 30 years old, with antecedents of two hepatic cysts resections, without knowing the histopathological diagnosis. She presented pain in the right hypochondrium and epigastrium, nausea, dyspepsia, and postprandial plenitude. Hepatic ultrasound revealed a large anechoic lesion, multiloculated, located in the right hepatic lobule. Hepatic cystectomy was performed. Histopathological diagnosis: Hepatobillary cystadenoma with mesenchymal stroma.
Conclusion: Hepatic polycystic disease is characterized by the presence of multiple variably sized cysts, is autosomically dominant, and is frequently associated to renal polycystic disease. The cystadenoma with mesenchymal stroma is described as a multiloculated cyst, covered by a columnar or cubic epithelium and a subjacent mesenchymal stroma, surrounded by a pseudocapsule of connective tissue that separates them from the adjacent parenchyma.
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