González RLA, López CG, Castillo AJ, Rascón AA, Pérez MT, Ruiz BNP

Language: Spanish
References: 11
Page: 9-14
PDF size: 561.49 Kb.

ABSTRACT

Introduction. Truncus Arteriosus type I is a rare heart malformation. This malformation is characterized by the presence of a single arterial vessel arising from the base of the heart and giving origin to the coronary, systemic and pulmonary arteries. Material y Methods. We reviewed clinical records and registered interesting clinical variables. We obtained the chest x-ray and EKG for their analysis. Two echocardiography studies were reviewed and the other two in autopsy report. Results. We found four cases with truncus arteriosus type I diagnostic. Two of them had genetics syndrome and symptoms of respiratory distress and cyanosis. They develop signs of heart failure and pulmonary infection. The specific diagnostic was made with echocardiogram in two cases and the other ones in autopsy. Conclusion. Even though this heart malformation is less frequent, we have to keep in mind that it could present early clinical signs at birth; echocardiogram study is a specific diagnostic in the variety of truncus arteriosus. Without surgical treatment, besides the development of early high severe pulmonary pressure, most frequently complicates with pulmonary infection. Our experience is limited in four cases with clinical signs of congestive heart failure, and pulmonary infection with malnutrition. A genetic syndrome was present in two cases and anatomic anomaly was a tuncal valve regurgitation and atrial septal defect. The diagnosis of this variety of this truncus arteriosus was established by echocardiogram.

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