Prieto-Díaz-Chávez E, Medina CJL, Casillas MR, Ávalos GJ, Trujillo HB

Language: Spanish
References: 12
Page: 231-233
PDF size: 140.33 Kb.

ABSTRACT

Introduction: Hirschsprung’s disease or primary megacolon is an unusual condition that presents a frequency rate of one in 5,000 births. In newly-born babies, low intestinal obstruction is often associated to certain disorders such as Hirschsprung’s disease. In adult people, this mentioned disease is unusual and it must be suspected in cases of constipation refractory to treatment. The treatment is usually surgical, with the intestinal segment commonly innervated to the anal canal. Objective: To present a case from an adult subject having a condition of constipation refractory to management. This patient was subjected to surgical management. A case-presentation: Male individual being 18 years old presenting constipation refractory since his childhood. The colon revealed megacolon through an enema. The patient was subjected to laparotomy, finding a rectum larger than 15-cm diameter, performing subtotal cholectomy with low anastomosis. Conclusions: Hirschsprung’s disease is an unusual condition.

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