2009, Number 2
Marsupialization and external drainage: Effective procedure for giant hamartoma of the liver in children
Silva-Báez H, Riojas-Robles J, Pelayo M, Coello-Ramírez P
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Language: Spanish
References: 11
Page: 167-170
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ABSTRACT
Introduction. Hamartoma of the liver is a benign tumor that develops from the portal triad. It is characterized by a cystic benign mass in the biliary tree. Maresch in 1903 made the first description of this entity as a mesenchymal tumor or biliary fibroadenoma. Edmondson in 1956 named this entity mesenchymal hamartoma. Treatment consists in radical excision of the lesion; this is not always possible and other options for treatment have been described such as enucleation, marsupialization, sequential resection, drainage, embolization and transplantation.Case reports. Three pediatrics patients were diagnosed with a tumor-cyst like lesion in the liver by computed tomography and abdominal ultrasound. Diagnosis was confirmed by histopathology as benign hamartoma of the liver. Treatment consisted in marsupialization and external drainage. Eight weeks later, a computed tomography scan was performed in each case showing a complete resection of the lesion substituted by fibrosis.
Conclusion. Mesenchymal hamartoma of the liver in children is a challenge for pediatric surgeons due to high rate of complications after resection of the tumor. We propose this technique as an alternative for treatment.
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