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Órgano Oficial de la Asociación Mexicana de Hepatología

2009, Number 2

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Ann Hepatol 2009; 8 (2)

Congenital choledochal cyst in an infant with cystic fibrosis

Tabatabaie P, Gholam-Hossein F, Farahmand F, Eftekhari K, Ahmadi M, AhmadF, Bazvand F, Rezaei N

Language: English
References: 10
Page: 156-157
PDF size: 106.85 Kb.


Text Extraction

Congenital choledochal cyst is malformation of the biliary ductal system, which rarely occur. We describe here a 4-month old boy, who was referred to our center with respiratory distress and low level consciousness. In physical examination, a mass was detected in right upper quadrant of abdomen. Sonographic examination indicated a cystic structure representing the choledochal cyst. Further evaluation confirmed the diagnosis of cystic fibrosis in this patient. Although choledochal cyst is considered as a rare disease, it is the most frequent malformation of the extrahepatic biliary ducts, which easily could be misdiagnosed.


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