Lazcano-Gómez G, Fuentes-Cataño C, Villanueva-Mendoza C

Language: Spanish
References: 14
Page: 49-54
PDF size: 86.38 Kb.

ABSTRACT

Objectives: To identify the abnormalities of the visual sensory system related more frequently with congenital or infantile nystagmus, also to identify the prevalence of sensory and motor congenital nystagmus. Methods: Patients with congenital nystagmus were examined from the Clinic of Strabismus, Asociación para Evitar la Ceguera en México. According to the clinical features the congenital nystagmus was classified as sensory or motorcongenital nystagmus. In patients without a definitive diagnosis, slit lamp examination, genetic evaluation andcomplementary studies were provided to obtain the cause of nystagmus. Results: 63 patients with congenital nystagmus were evaluated between 3 months and 12 years of age. We identified 34patients with abnormal ocular findings and diagnosis of sensory congenital nystagmus, 10 patients without visual sensorydisorders were diagnosed as motor congenital nystagmus and 3 patients as neurologic nystagmus. In 12 patients we were not able to determine the cause of nystagmus. Conclusions: The evaluation of patients with congenital nystagmus must include: family history, decreased visual acuity, abnormal color vision, photophobia, nyctalopia, fundus evaluation (direct and indirect ophtalmoscopy). The most useful tests in these patients are: electroretinography, visual evoked potentials and color vision.

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