González GE, Bernal DV, Villarreal ZM

Language: Spanish
References: 18
Page: 148-153
PDF size: 279.62 Kb.

ABSTRACT

Heart primary malignant tumors are rare, three-quarters of these are sarcomas. The clinical manifestations are nonspecific and usually occur in tumor at advanced stages; dyspnea is the most frequent symptom, which may accompany angina, dizziness, syncope and systemic manifestations such as loss weight and fever, often suspecting other diseases and delaying diagnosis. Owing to, and that there are reports of specific histopathology variants with small populations, at present there is not a consensus in the therapeutic modality for cardiac sarcomas. The first line treatment is complete surgical resection of the sarcoma. The prognosis of these injury remains grim, despite improve diagnostic with technological advances and adjuvant chemotherapy. We present the case of a patient that ended in primary cardiac leiomyosarcoma with low-grade malignancy, which remains in surveillance and treatment with chemotherapy.

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