2009, Number 6
Acta Pediatr Mex 2009; 30 (6)
Baeza-Herrera C, Arcos-Aponte A, Suárez-Estrada C, García-Cabello LM, Piña-Perales JJ
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ABSTRACTIntroduction. Spontaneous prenatal closure of a gastroschisis is rare; it is usually associated with atresia of the midgut. This anomaly is known as “closed gastrochisis”. In Spanish we suggest the term antenatal paraumbilico-intestinal strangulation (APIS) or Grosfeld´s syndrome.
Material and method. A two-year review of 58 gastroschisis patients, identified four infants with this uncommon complication.
Results. In these infants the extracorporeal midgut was invariably necrotic or fibrotic. The remnant midgut was surgically removed; during the procedure we observed jejunal atresia of 35 to 40 cm and atresia of the left colon. All patients developed short bowel syndrome and three of them died at less than four weeks of age.
Conclusions. This series shows that this complication is potentially lethal.