López HJF, García RR, Sánchez VG, Pérez ZMA

Language: Spanish
References: 15
Page: 78-82
PDF size: 140.49 Kb.

ABSTRACT

Congenital hydrocephaly is a difficult diagnostic problem, attributable to no hereditary causes, the genetical agents are important, the physiopathologic findings and the subsequent medical management and advices to the parents can confuse its determination. Specifically when uncommunicative congenital hydrocephaly is the result of aqueductal stenosis, other abnormalities association with congenital hydrocephaly must be considered aside; as Dandy-Walker’s Syndrome case. Dandy-Walker’s Syndrome is a malformation of the fourth ventricle and cerebella vermis hypoplasia due to a vermis developmental defect before the embryological differentiation, clinical manifestations tend to prove theirselves during lactation because of skull growing in a progressive way due to hydrocephaly essentially, another congenital encephalic malformations of neuronal migration upsets can appear; the treatment is the ventricles derivation.

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