García-Juárez JD, Tohen-Bienvenu A, Jiménez-Cabuto IC, Molina-Méndez J

Language: Spanish
References: 6
Page: 126-129
PDF size: 775.31 Kb.

ABSTRACT

Introduction: Klippel-Tranaunay syndrome is a rare congenital condition characterized by skin angiomas with arteriovenous malformations and hypertrophy of the soft and bone tissues of one extremity. The clinical case presented herein involved total hip replacement due to arthrosis secondary to avascular necrosis of the femoral head, which resulted in the hypervascularity that occurs with this syndrome. A 37 year-old female was diagnosed with grade IV hip arthrosis and Klippel-Trenaunay syndrome. Laboratory and imaging tests were performed to determine the local conditions for the surgical approach to the hip. The preoperative MR angiography identified the arteriovenous malformation tract to determine the limits of the approach.Discussion: The arteriovenous malformations that occur in this syndrome turn the approach into a challenging one due to the potential bleeding, thus extreme prophylactic and technical measures must be applied. There are very few reports in the literature on this treatment.

REFERENCES

1. Martínez-Gimeno E, Allende-Riera AJ: Síndrome de Klippel-Trenaunay y gammagrafía ósea. A propósito de un caso. Rev Esp Med Nucl 2006; 25: 26-30.

2. Jane-Lisko H: Trenaunay – Weber Departamento de Dermatología, Universidad de Minnesota Medical School. Octubre 2006.

3. Avellaneda M: Síndrome de Klippel-Trenaunay, Instituto de Salud Carlos III Diciembre 2003.

4. Mallick A, Weeber A: An experience of arthroplasty in Klippel-Trenaunay syndrome. Eur J Orthop Surg Traumatol 2007; 17: 97-9.

5. Willis-Owen CA, Cobb JP: Artroplastía total de cadera en el síndrome de Klippel-Trenaunay. An Real Col Ciruj Ingl 2008; 90(8): 6-8.

6. Leal J, Davies AP: Knee arthroplasty in Klippel-Trenaunay syndrome. A case presentation with 5 years follow-up. J Arthropl 2008; 23: 623-6.