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2011, Number 4

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Med Cutan Iber Lat Am 2011; 39 (4)

Segmental Darier disease type 1

Álvarez LMÁ, Garnacho SG, Salido VR, Rangel MY, Moreno GJC, Vélez GNAJ

Language: Spanish
References: 15
Page: 187-189
PDF size: 813.01 Kb.


ABSTRACT

Segmental Darier disease is an unusual form of this condition. It is characterized by the localized distribution of the lesions along Blaschko´s lines. A genomic mosaicism has been recently demonstrated in these patients. Both type 1 and type 2 mosaic phenotypes have been reported.
We report a case in which clinical and histological findings were consistent with type 1 segmental Darier disease and we include a revision on the subject.


REFERENCES

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