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Colegio de Medicina Interna de México.
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2012, Number 2

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Med Int Mex 2012; 28 (2)

Situs inversus totalis

Carrillo ER, Arias DCR, Huacuja BRR, García GM, Carrillo CCA, Carrillo CDM
Full text How to cite this article

Language: Spanish
References: 13
Page: 187-191
PDF size: 356.86 Kb.


Key words:

Dextrocardia, Embryology, Situs Inversus Totalis.

ABSTRACT

Situs inversus is an uncommon disease. It is a congenital abnormality during embryonic development, which affects the establishment of left-right axis with the consequent conversion in mirror image of all pair organs. We report the case of a 17-year-old female who was admitted to the Intensive Care Unit, diagnosed with diabetic ketoacidosis. During physical examination we diagnosed dextrocardia with situs inverus totalis, and it was corroborated by additional exams such as electrocardiogram and imaging studies. The early diagnosis and treatment of this entity avoids the risk of diagnosis and therapeutic errors.


REFERENCES

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  4. Adeyekun AA, Onunu AN, Mazeli FO. Dextrocardia with Situs Inversus: A case report. West Afr J Med 2003;22:358-360.

  5. Sadler TW. Desarrollo temprano: Desde la fecundación hasta la gastrulación. En: Langman. Fundamentos de embriología médica con orientación clínica, Buenos Aires: Panamericana, 2006;5-14.

  6. Carlson B. Formación de las capas germinales y sus primeros derivados. En: Embriología humana y biología del desarrollo, 4a ed. Barcelona: Elsevier, 2009;85-102.

  7. Piryani RM, Shukla A, Prasad DN, Kohli SC, Shrestha G, Singh D. Situs inversus with dextrocardia with multiple cardiac lesions in adult. Kathmandu Univ Med J 2007;5:247-249.

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  11. Gindes L, Hegesh J, Barkai G, Jacobson JM, Achiron R. Isolated levocardia: prenatal diagnosis, clinical importance, and literature review. J Ultrasound Med 2007;26:361-365.

  12. Fung TY, Chan DL, Leung TN, Leung TY, Lau TK. Dextrocardia in pregnancy: 20 years' experience. J Reprod Med 2006;51:573-577.

  13. Kinney TB, DeLuca SA. Kartagener's syndrome. Am Fam Physician 1991;44: 133-134.




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Med Int Mex. 2012;28