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>Journals >Acta Pediátrica de México >Year 2012, Issue 5


Mata-Pérez K, Teja-Ángeles E, Durán-Gutiérrez LA
Oral rehabilitation under general anesthesia in a boy with Hallervorden-Spatz syndrome. Report of a case
Acta Pediatr Mex 2012; 33 (5)

Language: Español
References: 25
Page: 227-231
PDF: 208.05 Kb.


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ABSTRACT

Hallervorden-Spatz syndrome is a rare neuro-degenerative disorder characterized by high levels of iron deposits in the brain. Patients exhibit extrapyramidal and cognitive impairment and dystonia, seizures, spasticity, dysarthria, rigidity of limbs and visual disturbances. We report a case of a patient with this syndrome, who had multiple carious lesions and self-inflicted injuries of the mucosa of the lower lip and tongue, produced during periods of intense orofacial spasms. Oral rehabilitation was performed under general anesthesia. Dental treatment was given to promote dental hygiene, pain relief, and elimination of infections.


Key words: Hallervorden-Spatz syndrome, neurodegenerative disease, orofacial spasm, self-inflicted injuries, oral rehabilitation.


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>Journals >Acta Pediátrica de México >Year 2012, Issue 5
 

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