Calzada AJL, Jaramillo RH, Delgadillo MG, Macías DDM

Language: Spanish
References: 25
Page: 504-507
PDF size: 226.75 Kb.

ABSTRACT

Wegener's granulomatosis is a necrotizing granulomatous vasculitis that affects the upper respiratory tract, lower and glomeruli. This and microscopic polyangiitis are vascular diseases associated with neutrophil cytoplasmic antibodies (ANCA). Wegener's granulomatosis is a rare disease, cause not yet defined, with an incidence of 0.4 cases per 100,000 inhabitants. We report the case of a female patient of 15 years old, no medical history of importance but with C3 and C4 report normal, positive ANA and positive c-ANCA 1:40. The literature review updates the knowledge about this disease that allow the clinician to diagnose keep it in mind to try.

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13. Mender M, Díaz A. Granulomatosis de Wegener. Tratamiento. Revista de posgrado de la VI cátedra de medicina 2005;44:21-23.

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