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Boletín Médico del Hospital Infantil de México

2012, Number 6

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Bol Med Hosp Infant Mex 2012; 69 (6)

Acrodermatitis enteropathica

Toxtle RMA, Hernández AAE

Language: Spanish
References: 15
Page: 475-480
PDF size: 237.25 Kb.


ABSTRACT

Background. Acrodermatitis enteropathica is a rare but easy to manage condition but with great clinical relevance. The condition must be diagnosed properly and timely. We present an infant with the following clinical triad: acral dermatitis, diarrhea and alopecia. Zinc treatment should be initiated, even from a primary care level. Clinical response is immediate and without sequelae.
Case report. We present the case of an infant with chronic malnutrition, short stature, psychomotor retardation and large symmetrical scaly skin lesions with disseminated alopecia totalis. The patient was admitted to the Hospital Regional de la Huasteca, Huejutla, Hidalgo. Acrodermatitis enteropathica was suspected in the clinic and serum zinc and skin biopsy were carried out. Clinical improvement was obtained from the first 2 weeks of treatment.
Conclusions. Treatment initiation with zinc sulfate at a dose of 2-5 mg/kg/day has immediate clinical implications with complete symptom remission.



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