Cabezas PMA, Pérez GR, Argíz MA, Quintero MY

Language: Spanish
References: 9
Page: 173-178
PDF size: 117.40 Kb.

ABSTRACT

Periparturient hemorrhages are the leading cause of extremely serious maternal morbidity and maternal death in Cuba and the world. Acquired Hemophilia A is a rare bleeding disorder characterized by the presence of antibodies against circulating factor VIII (FVIII). We present the case of a 36 years old pregnant woman with term pregnancy and vaginal delivery that suffers from hemorrhagic manifestations in the immediate postpartum secondary to raffia hematoma, requiring blood transfusion. Then she presents a bruise in the right upper limb secondary to stroke that requires surgical repair. The postpartum torpid evolution characterized by sustained bleeding raffia and the surgically treated arm, makes us suspect of the presence of a blood disorder. We observed a decrease in the FVIII factor, which involves the diagnosis of acquired hemophilia and requires treatment with recombinant VIIa factor (FVIIar) concentrate and cyclophosphamide. Posterior evolution was favorable. The patient was discharged without sequelae.

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