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2012, Number 12

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MediSan 2012; 16 (12)

Hailey - Hailey disease in several generations of a family

López PN, Tablada RME, López OD, Selva LV, Solá OA
Full text How to cite this article

Language: Spanish
References: 11
Page: 1936-1941
PDF size: 272.13 Kb.


Key words:

benign familial pemphigus, Hailey-Hailey disease, genodermatosis, dermatology ward, secondary health care.

ABSTRACT

Two case reports of adult siblings are described, who presented with benign familial pemphigus or Hailey-Hailey disease - type of genodermatosis by altered epidermal cohesion - attended in "Dr. Juan Bruno Za yas Alfonso" Teaching General Hospital of Santiago de Cuba. Patients were treated with steroids at anti-inflammatory doses, antibiotics, and topical plant liniment and aloe cream, besides receiving flower therapy. In general, both of them improved the clinical pict ure during their stay in this institution.


REFERENCES

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  10. Bessa GR, Grazziotin TC, Manzini AP, Weber MB, Bonamigo RR. Hailey-Hailey disease treatment with Botulinum toxin type A. An Bras Dermatol. 2010; 85(5): 717-22.

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