Guerrero-Galindo R, Castrejón E, Aguirre-Portillo L, Cervantes-Michel JL, Espejo-Plascencia I

Language: Spanish
References: 12
Page: 247-249
PDF size: 83.95 Kb.

ABSTRACT

Hemangioblastoma is a benign neoplasm highly vascularized of the central nervous system and is present between 2 to 3% of intracranial tumors in adults, most often located in cerebellum in two thirds and the rest in brain stem, rarely in spinal cord. In most cases appear spontaneously; only 30 % of them are associated with Von Hippel Lindau disease. The peak incidence of intramedullary lesions is the fourth and fifth decade of life and affect both sexes equally. Most medullar tumors are located in the thoracic segment and are solitary lesions. The histogenesis is not well known, the initial symptoms are radicular pain, sensory or motor deficit slowly progressing according to the level of medulla involvement. The diagnosis is based on neurological examination and MRI of the spine. The definitive treatment is surgery for total removal. The radio and chemotherapy have no effect. Metastases are uncommon. Presented the case of male patient 25 years with a solid intramedullary hemangioblastoma of a year of evolution with partial spinal cord injury, underwent surgery with total removal of the tumor and postoperative neurological improvement.

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