Delgado HC, Mandizábal GR, Delgado OMA, Muñoz BJA, Jiménez JM, Monroy SA, Reyes SG

Language: Spanish
References: 0
Page: 88-93
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ABSTRACT

Craniosynostosis is a disorder of the skull shape caused by a premature fusion of the sutures. Together with other anomalies, it constitutes a syndrome. Craniosynostosis is pathology of heterogenic etiology. There are more than 90 syndromes of craniosynostosis known, excluding the occasional and secondary craniosynostosis. The diagnosis is made clinically and radiologically and the prevalence of all types is 1 O 1 6 for every 100,000 new born in the EUA. The most frequent synostosis is the fusion of the sagital suture foillowed by the fusion of the coronal. The premature fusion of the metopic and lambdoid sutures is less frequent. Cases of isolated craniosynostosis are sporadic. Craniosynostosis in the offspring is related to father's old age. In this paper, we will make a revision of anterior plagiocephaly with principal focus in the surgical technique, with detail in the surgical procedure. This revision is because of the importance of a precise diagnosis, since patient handling and treatment depend on it. lt is also important in order to provide proper genetic counseling about the possible complications such as: mental retardation, cardiac malformations and others (depend ing on the syndrome) and to inform the risk of recurrence in the family.