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Revista Mexicana de Angiología

Órgano Oficial de la Sociedad Mexicana de Angiología y Cirugía Vascular
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2008, Number 1

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Rev Mex Angiol 2008; 36 (1)

Síndrome de Klippel-Trenaunay-Weber. Reporte de un caso

Candia RRF, Palacios SJM, Candia GR, Rosas BR
Full text How to cite this article

Language: Spanish
References: 15
Page: 30-34
PDF size: 303.73 Kb.


Key words:

Cutaneous capillary Hemangioma, Hypertrophia, varicose osteohypertrophic nevus, deep arteriovenous fistulas.

ABSTRACT

The vascular congenital abnormalitys are difficult to classify by the similar clinical symptomatology in each one of them. The syndrome of Klippel Trenaunay (SKT) is defined by the three classic symptoms, cutaneous capillary Hemangioma, underlying varicose veins and hypertrophia of soft weaves or bony weaves of an extremity. The first cases were described by Klippel and Trenaunay in 1900, by the name of varicose osteohypertrophic nevus and later Weber in 1918 communicated other three patients with such associated clinical findings to deep arteriovenous fistulas, reserving for the se the name of syndrome of Klippel Trenaunay Weber or Parkes Weber. We report a case of a female patient 21 years old who developed syndrome of Klippel Trenaunay Weber.


REFERENCES

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Rev Mex Angiol. 2008;36