Gutiérrez-Escobedo J, Jiménez-Urueta PS, Castañeda-Ortiz RA, Ávila-Zaragoza LM, Shoup-Fierro CL, Salgado-Aiday M

Language: Spanish
References: 8
Page: 129-133
PDF size: 502.21 Kb.

ABSTRACT

Introduction: Congenital bilobar emphysema is an infrequent congenital malformation which may be the cause of respiratory insufficiency in the smaller suckling child. It is produced by the overexpansion of one lung lobe with compression of the normal lung parenchyma and displacement of the mediastinum bilobar or multifocal involvement is extremely rare. Our purpose is to present one cases of this illness which were surgically treated by our team. Case presented: A male infant developed respiratory distress at 4 months of age. He was born at term by abdominal delivery. The patient was hemodynamically stable, tachypneic, but with no abnormal lung sounds. Chest radiography demonstrated a hyperinflated left hemithorax with mediastinal shift to the right and mediastinal hernia. Surgery and histology examination demonstrated distended alveoli. He has been followed for 2 years and no complications have occurred since. Discussion: Congenital bilobar emphysema is a rare condition. Diagnosis of bilobar involvement may be difficult. Congenital bilobar emphysema may be managed by simultaneous or sequential bilobectomies. Surgical management should be guided by clinical and radiologic findings and evaluated peroperatively and postoperatively. Surgical management of bilobar emphysema is controversial.

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