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ISSN 1727-897X (Electronic)

2013, Number 3

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Medisur 2013; 11 (3)

Fronto-nasal Encephalocele. A Case Report

Ferrer MR, Ramírez RE, Segura LM, González RMR

Language: Spanish
References: 10
Page: 315-318
PDF size: 133.84 Kb.


ABSTRACT

Encephalocele is a herniation of the brain tissue through a congenital or acquired defect of the skull. The congenital condition is caused by a neural-tube defect attributable to an interaction among several genes and environmental factors. Anterior encephalocele is a rare entity and its incidence varies depending on the geographic area. We report the case of a newborn with a tumour protruding through the fronto-nasal region with a central pedunculated polypoid formation, in addition to the presence of bilateral cleft lip and palate. Surgical treatment was decided after consulting the Neurosurgery Department. This case report is interesting due to the rarity of this entity.


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