Lara-Sánchez C, González-Gutiérrez JC, Lara-Sánchez H, Mancera-Sánchez J, Hernández-Calleros J

Language: Spanish
References: 8
Page: 529-532
PDF size: 228.36 Kb.

ABSTRACT

Background: Autoimmune pancreatitis (AIP) type 1 is a systemic disease which presents as a lymphoplasmacytic sclerosing pancreatitis. Its presentation is seen more commonly in men, and other organs can be affected because of their infiltration with positive plasmatic cells for IgG4.
Clinical case: We present the case of a 44-year-old woman with a history of Sjögren's syndrome, a clinical profile characterized by 3 months of generalized jaundice and weight loss of 5 kg, with a presumptive diagnosis of pancreatic carcinoma. An endoscopic ultrasound-guided core needle biopsy. (EUS-TACB) was performed taking biopsies of a pancrea's head lesion. The histopathological study revealed, along with most of the HISORt criteria, an AIP type 1.
Conclusions: AIP is a rare disease whose research and understanding are evolving, therefore a prepared medical team, familiarized with the disease is needed for a proper diagnosis. A diagnosis and satisfactory therapeutic management was realized during the evolution of the disease, thus avoiding an unnecesary surgery.

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