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ISSN 1684-1824 (Electronic)

2013, Number 5

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Rev Méd Electrón 2013; 35 (5)

Hemobile as an unusual presentation form of the Caroli´s disease

Fernández HL, Ávila AD, Arredondo BA, Heredia CAA

Language: Spanish
References: 11
Page: 509-515
PDF size: 476.31 Kb.


ABSTRACT

Caroli´s disease, or communicant ectasia of the intrahepatic biliary ducts, is a congenital entity, characterized by multiple saccular or cystic dilatations of the intrahepatic biliary ducts. In this work we present a new case of a carrier of Caroli’s disease. It deals with a female patient, aged 26 years, with antecedents of good health status, who entered the hospital with high fever of 39oC, painful hepatomegaly and hyper echoic images in the liver, detected in the ultrasonography, with slightly raised hepatic aminotranferases. During the second staying in the hospital she suffered fever complications and high digestive bleeding caused by important hemobile that compromised the hemodynamics and together with sepsis caused her to die. The patient entered the hospital because of cholangitis and presented an important hemobile leading her to hemodynamic complications, ascendant cholangitis, and finally a generalized sepsis as death cause.


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