Rottier SR

Language: Spanish
References: 12
Page: 411-415
PDF size: 173.20 Kb.

ABSTRACT

Familial hypertrophic cardiomyopathy is an inherited cardiac muscle disorder disease that affects sarcomeric proteins, resulting in left ventricular hypertrophy with predominant involvement of the interventricular septum in the absence of other causes of hypertrophy. It is characterized by a heterogeneous clinical and morphologic expression, complex pathophysiology,and diverse clinical course, being sudden death the most dreaded course of this disease.For which risk stratification and prevention with implantable cardioverter defibrillator are the recommended management for this patients. Descriptores: miocardiopatía hipertrófica, muerte súbita, gradiente de obstrucción subaórtico, cardiodesfibrilador implantable.

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