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2013, Number 4

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Rev Mex Anest 2013; 36 (4)

Noonan syndrome and malignant hyperthermia risk: total intravenous anesthesia for pediatric outpatient surgery

Ramírez-Paesano CR, Hachoue-Saliba ZS

Language: Spanish
References: 19
Page: 314-318
PDF size: 245.88 Kb.


ABSTRACT

The Noonan syndrome is a clinical entity that could be confused or related to other syndromes associated with the development of malignant hyperthermia. In order to avoid the appearance of a malignant hyperthermia crisis, the anesthetic technique should be free of triggering agents and patients should be adequately monitored. In this report we describe a child patient with probable Noonan syndrome and anesthetic management to cryptorchidism repair.


REFERENCES

  1. Benca J, Hogan K. Malignant hyperthermia, coexisting disorders, and enzymopathies: risks and management options. Anesth Analg. 2009;109:1049-1053.

  2. Tartaglia M, Gelb B, Zenker M. Noonan syndrome and clinically related disorders. Best Pract Res Clin Endocrinol Metab. 2011;25:161-179.

  3. Aggarwal V, Malik V, Malhotra KP, Kiran U. Noonan syndrome: an anesthesiologist’s perspective. Annals Cardiac Anaesthesia. 2011;14:214-217.

  4. Bentires AM, Kontaridis MI, Neel BG. Stops along the RAS pathway in human genetic disease. Nat Med. 2006;12:283-285.

  5. Tidyman WE, Rauen KA. The RAS apathies: developmental syndromes of RAS/MAPK pathway dysregulation. Curr Opin Genet Dev. 2009;19:230-236.

  6. Litman R. Management of malignant hyperthermia and malignant hyperthermia–susceptible patients in the ambulatory setting. ASA Refresher Courses in Anesthesiology. 2011;39:86-91.

  7. Lee CK, Chang BS, Hong YM, Yang SW, Lee CS, Seo JB. Spinal deformities in Noonan syndrome: a clinical review of sixty cases. J Bone Joint Surg. 2001;83:1495–1502.

  8. Hunter A, Pinsky L. An evaluation of the possible association of malignant hyperpyrexia with the Noonan syndrome using serum creatine phosphokinase levels. J Pediatr. 1975;86:412-415.

  9. D’Arcy CE, Bjorksten A, Yiu EM, et al. King-Denborough syndrome caused by a novel mutation in the ryanodine receptor gene. Neurology. 2008;71:776–777.

  10. Noonan syndrome guideline development group. Management of Noonan syndrome-a clinical guideline[Internet]. UK: University of Manchester DYSCERNE; 2010 [Accessed 25 July 2011].

  11. Mani V, Morton N. Overview of total intravenous anesthesia in children. Pediatric Anesthesia. 2010;20:211-222.

  12. McCormack J. Total intravenous anesthesia in children. Current Anaesthesia & Critical Care in Press. 2008;1-6.

  13. Wilson G. Target controlled infusion anesthesia in children. S Afr J Anaesthesiol Analg. 2010;16:124-126.

  14. Ong C, Seymour R, Lirk P, Merry A. Combining paracetamol (acetaminophen) with nonsteroidal antiinflammatory drugs: a qualitative systematic review of analgesic efficacy for acute postoperative pain. Anesth Analg. 2010;110:1170-1179.

  15. Zaragoza LG, Mejía TG, Peralta ZE. Bloqueo de nervios periféricos guiados por ultrasonido. Rev Mex Anestesiol. 2008;31:282-297.

  16. Bermúdez E. Bloqueos de la pared abdominal. Rev Chil Anest. 2011;40:230-237.

  17. Suresh S, Chan V. Ultrasound guided transverses abdominis plane block in infants, children and adolescents: a simple procedural guidance for their performance. Pediatric Anesthesia. 2009;19:296-299.

  18. Siddiqui M, Sajid M, Uncles D, Cheek L, Baig M. A meta-analysis on the clinical effectiveness of transverses abdominis plane block. Journal of Clinical Anesthesia. 2011;23:7-14.

  19. Klockars J, Hiller A, Ranta S, Talja P, van Gils M, Taivainen T. Spectral entropy as a measure of hypnosis in children. Anesthesiology. 2006;104:708-717.




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