Uribe OJS, Palomera GHG, Quillo OJ, Alcántara GLA, Zambrano VLE, Gómez LE, González PEA, Paz GJ, Ramírez JJC, Velázquez SH

Language: Spanish
References: 12
Page: 477-481
PDF size: 1183.18 Kb.

ABSTRACT

Background. The Ewing sarcoma family includes Ewing bone sarcoma, primitive neuroectodermal tumor, extraosseous Ewing’s sarcoma, and Askim tumor (Ewing sarcoma of the chest wall). The most common sites of these tumors are chest and limbs. These malignancies arise from bone or soft tissues. Histologically, tumors are characterized by high cellularity and are small, round, blue and with a tendency to form rosette structures.
Case report. We report the case of a 14-year-old patient whose evolution began 3 months before admission with left frontoparietal headache radiating to the orbit. During neurological examination, proptosis and decreased visual acuity were found as well as papillary atrophy. Cranial computed tomography identified a left intraorbital injury and another ipsilateral temporoparietal. Tumor exeresis was performed, reporting positive for primitive neuroectodermal tumor markers, vimentin and CD99.
Conclusions. Ewing sarcoma is extremely rare at the orbital level; however, it is prudent to consider this tumor as a differential diagnosis in lesions of this region. Prognosis depends on early diagnostic accuracy.

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