Pila PRV, Pila PRU, Rosales TP, Artola GJA

Language: Spanish
References: 12
Page: 134-145
PDF size: 273.82 Kb.

ABSTRACT

Background: Behçet's disease is a rare disease of world proportions that affects males in the third and fourth decades of life. Clinical manifestations, etiopathogenic theories, diagnoses and treatments were reviewed.
Objective: to present a case of Behçet's disease with multisystemic manifestations which constitutes the first case reported in the province of Camagüey.
Clinical case: a forty-five-year-old, mixed-race patient, who works in the gastronomy sector without any personal records of interest, appears with around five years of suffering from ocular injuries caused by recurrent conjunctivitis and uveitis, as well as maculopapular lesions in the skin, arthritis without functional impotence, and diarrhea in certain occasions. Six months ago, the patient started presenting aphthous ulcers, followed by genital ulcers. The patient also noticed a weight loss of 10 kg in the last two months and had suffered from headaches, depression and serious personality disorders. All the studies were normal except for the erythrocyte sedimentation rate and the C-reactive protein. The pathergy results were positive with 5 mm, as well as the histopathological studies which confirmed the diagnosis of vasculitis caused by this disease. The therapy applied greatly improved the patient’s condition who was discharged from hospital 38 days later but kept the prednisone support treatment (10 mg) in order to avoid neurological complications which are the most serious.
Conclusions: Behçet's disease has a great importance nowadays because it resembles other diseases from the clinical, etiological, and therapeutic points of view.

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