Ordoñez GR, Ruiz MM

Language: Spanish
References: 8
Page: 119-121
PDF size: 680.58 Kb.

ABSTRACT

Ewing sarcoma / primitive neuroectodermal tumor is a rare neoplasm that belongs to the family of tumors of small round blue cells, affects men and women with a male / female ratio of 1.5:1 and have a peak incidence between 10 and 20 years. Its classic histology look with a high cellularity, composed of small, round and compact cells, giving a bluish appearance like a diffuse type lymphoma, which has served to call these also “small, round and blue cell tumors”, because stain intensely with hematoxylin. Histological diagnosis is supported by immunohistochemistry with CD99 marker and cytogenetic demonstration of the translocation 11:22. It very rarely occurs in the nasal cavity. For localized Ewing tumor, treatment usually begins with chemotherapy and if this is given at the right time, the 5-year survival can be 60 to 70%.

REFERENCES

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