Santos PA, Mirabal OJA, Valero HA, Alonso JI

Language: Spanish
References: 10
Page: 37-41
PDF size: 787.28 Kb.

ABSTRACT

Ehlers-Danlos syndrome is an uncommon finding in clinical practice and is characterized by a series of hereditary disorders of connective tissue. Some patients present with cardiovascular repercussions and the structure most commonly affected is the mitral valve, on many occasions requiring valve replacement surgery. A 51 year old patient presents with a diagnosis of Ehlers-Danlos syndrome with a sever mitral valve prolapsed and repeated episodes of infectious endocarditis. Due to their clinical deterioration a prosthetic mechanical valve replacement surgery is decided upon. Clinical and intracardiac hemodynamic parameter improvements were shown after the surgery was applied, with a minimum of postoperative complications.

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