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2014, Number 1

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Rev Cubana Pediatr 2014; 86 (1)

Esophageal atressia-associated congenital anomalies

Reyes RR, Muñiz EJ, Polo AI, Alvaredo SMA, Armenteros GA, Hernández FNM

Language: Spanish
References: 17
Page: 68-76
PDF size: 96.20 Kb.


ABSTRACT

Introduction: esophageal atresia occurs in one out of 3 000 or 4 500 livebirths. Males are slightly predominant, but this is not a universal finding and maybe it is not valid for all varieties. With increasing survival rates of children operated on from esophageal atresia, the associated anomalies have become more significant since more than half of these children suffer one or more accompanying anomalies.
Objective: to characterize the esophageal atresia-associated anomalies.
Methods: an observational, cross-sectional and descriptive study of all the cases diagnosed with esophageal atresia, with or without tracheal esophageal fistula, from January 2000 to December 2011 was conducted in "José Luis Miranda" provincial pediatric teaching hospital in Santa Clara, Villa Clara province, Cuba.
Resultados: congenital cardiovascular anomalies were prevailing, followed by digestive and respiratory malformations. The most frequent one, together with interatrial communication, was anorectal malformation. There was a case of duodenal atresia as well as another case of diaphragmatic agenesis. There was no association between them. The patients with non-cardiovascular congenital anomalies are 2.1 times more likely to die than those unrelated to this type of anomaly. The global mortality rate for this series was 46.9 %.
Conclusions: the existence of congenital anomaly raises the mortality likelihood for these patients, mainly in cases of major non-cardiovascular and critical cardiovascular anomalies.


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