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ISSN 1561-3070 (Electronic)

2014, Number 1

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Rev Cub Oftal 2014; 27 (1)

Schnyder crystalline dystrophy

Guerra AM, Cambas AAA, de Prada SC, Parapar TSI, Averoft L, Lora DK

Language: Spanish
References: 18
Page:
PDF size: 87.54 Kb.


ABSTRACT

Central crystalline dystrophy known as Schnyder´s dystrophy, called like this because he was the first one to describe it in 1927 in Switzerland, is the main inherited entity with liquid deposits in the corneal stroma. This disease is characterized by white-yellow deposits into the central and superficial corneal stroma. A 28 years old black male patient, with previous history of health problems, went to the doctor´s office and mentioned visual reduction and progressive coloring changes in both eyes that had lasted some years. Ophthalmologic examination of both eyes showed annular white lesions at the corneal stroma, with light central corneal haze. Simple hypermetropic astigmatism was detected in the refractive exams. The rest of ophthalmologic exams was negative. For more secure diagnosis, confocal microscope was used. It was concluded that the patient had stromal corneal dystrophy, or Schnyder´s crystalline dystrophy.


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