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2014, Number 2

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Rev Mex Cardiol 2014; 25 (2)

Ebstein’s anomaly

Jordán-Ríos A, Magaña-Bailón E, Martínez-Aguilar M, Maury-Ordaz S, Juárez-Orozco LE, Jiménez-Niño A, Álvarez S, Alexánderson-Rosas E

Language: Spanish
References: 31
Page: 82-85
PDF size: 128.74 Kb.


ABSTRACT

Ebstein’s anomaly is a congenital malformation that is characterized primarily by abnormalities of the tricuspid valve and right ventricle, specifically tethering of the posterior and septal tricuspid valve leaflets to the right ventricle endocardium resulting in an apical displacement of tricuspid ring. The first reported case dates back to 1866 by Wilhelm Ebstein. Clinical presentation varies among patients. The most common symptoms are: progressive cyanosis, exertional dyspnea, heart failure, palpitations and arrhythmias. Patient approach should include electrocardiogram, chest X-ray and transthoracic echocardiogram, the latter being the gold standard for diagnosis. Only those patients who meet established criteria will undergo surgical treatment. Given the high similarity of Ebstein’s anomaly with other dysplasias of the tricuspid valve, it is essential to conduct a multidisciplinary evaluation to establish an accurate diagnosis and treatment.


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