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ISSN 1810-2352 (Print)

2012, Number 1

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Rev Cub Med Int Emerg 2012; 11 (1)

Mitral valve substitution in a patient with Ehlers-Danlos syndrome

Rondón AJ, Rodríguez SF, Díaz GI, García RR, Pupo SP, Suárez RA

Language: Spanish
References: 8
Page: 2385-2391
PDF size: 148.15 Kb.


ABSTRACT

The presence of a mitral valve prolapse could be to an alteration in the type III type collagen formation with a myxomatous degeneration and accumulation of mucopolysaccharides in mitral valves and sometimes in the subvalvular tract being the more frequent cardiovascular expression of the Ehlers-Danlos syndrome. To describe the anesthetic-surgical behavior of a patient with severe mitral insufficiency provoked by the above mentioned syndrome authors present the case of a patient aged 48 with a history of bronchial asthma and high blood pressure, treated with enalapril and in whom at 15 years old a systolic murmur in mitral focus being studied diagnosing this syndrome. Hi is operated on carrying out mitral valve substitution with mechanical prosthesis without complications. The mitral valvular prolapse is the more frequent cardiac expression of this unusual syndrome which with a timely surgical treatment expresses by general an appropriate clinical course.


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