2014, Number 3
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Acta Med Cent 2014; 8 (3)
Quincke's disease, challenge of the Specialist in Otorhinolaryngology
Rodríguez LM, Sarduy BL, Corrales ÁM
Language: Spanish
References: 10
Page: 136-140
PDF size: 65.70 Kb.
ABSTRACT
Quincke's disease or hereditary angioedema is a genetic disease caused by the
functional deficiency of the enzyme C1 inhibitor. It is a rare desease of
autosomal dominant transmission , characterized by recurrent self-limiting episodes of angioedema. Its incidence is estimated from 1:10 000 to 1:50 000
habitants, it has been described in all races and affects both sexes equally and
attacks affect the skin, abdomen and pharynx or larynx. Cuba, especially the
province of Villa Clara, have been affected in recent years by the presence of
patients suffering this disease. The rapid diagnosis, based on a proper physical
examination, and appropriate treatment are essential tools to avoid
complications. A call is made on the medical act in this health situation in order
to preserve the most precious treasure, life.
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